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Severe coronary artery ectesia in a paediatric patient with Noonan syndrome presenting for transcatheter pulmonary valve placement

Published online by Cambridge University Press:  13 January 2025

Christopher Herron Open the ORCID record for Christopher Herron [Opens in a new window] ,
Karen Iacono  and
David Nykanen
Christopher Herron*
Affiliation:
Department of Pediatric Cardiology, Arnold Palmer Hospital for Children, Orlando, FL, USA
Karen Iacono
Affiliation:
Department of Pediatric Cardiology, Arnold Palmer Hospital for Children, Orlando, FL, USA
David Nykanen
Affiliation:
Department of Pediatric Cardiology, Arnold Palmer Hospital for Children, Orlando, FL, USA
*
Corresponding author: Christopher Herron; Email: [email protected]
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Abstract

Coronary ectasia is a very rare phenomenon seen in Noonan syndrome with only a few documented case reports. We describe a 14-year-old with Noonan syndrome and tetralogy of Fallot with described coronary artery ectasia since infancy who presented for possible transcatheter pulmonary valve placement and was found to have severe ectasia of bilateral coronary arteries.

Keywords

Noonan syndromecoronary dilationpulmonary stenosis
Type
Images in Congenital Cardiac Disease
Information
Cardiology in the Young , Volume 35 , Issue 1 , January 2025 , pp. 192 - 194
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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References

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