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Pulmonary vasodilator-induced haemodynamic decline and recovery post-discontinuation in two single-ventricle cases

Published online by Cambridge University Press:  10 March 2025

Yuichi Ishikawa Open the ORCID record for Yuichi Ishikawa [Opens in a new window] ,
Yuki Iwaya  and
Ayako Kuraoka
Yuichi Ishikawa*
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
Yuki Iwaya
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
Ayako Kuraoka
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
*
Corresponding author: Yuichi Ishikawa; Email: [email protected]
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Abstract

Pulmonary vasodilators increased the systemic-to-pulmonary collateral flow in two single-ventricle cases, causing haemodynamic decline. Discontinuation reversed the collateral flow and improved heart failure, highlighting the need for careful monitoring. Serial cardiac MRI, as a non-invasive tool, may be essential to detect changes in collateral flow and guide vasodilator use for optimal management in this population.

Keywords

pulmonary vasodilatorsingle ventriclesystemic-to-pulmonary collateral flowcardiac MRItwo-dimensional phase contrastFontan
Type
Brief Report
Information
Cardiology in the Young , Volume 35 , Issue 3 , March 2025 , pp. 649 - 651
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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